Stargardt Disease (Stargardt Macular Dystrophy, Fundus Flavimaculatus)
-Polymorphic sheen in the macula which is generally ovoid in appearance,surrounding the fovea.
-F.A:* in the early stages of the disease will show a so-called “dark choroid” corresponding to the paramacular region and peripheral fundus, where there is accumulation of lipofuscin in the pigment epithelium which blocks choroidal fluorescence.
*A hyperfluorescence is seen where there is atrophy of the pigment epithelium.
-Some patients with Stargardt disease demonstrate flecks in the paramacular region, along the arcades and in the near peripheral fundus.
-Most common hereditary macular dystrophy. It is characterized by bilateral atrophy of the macula and underlying RPE, central vision impairment.