Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)

By posted on June 9, 2014 9:37AM
Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)

Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)

*The typical features include:
-Waxy pallor of the optic nerve.
-Narrowing of retinal arterioles
-A generalized mottling and moth-eaten pattern to the retinal pigment epithelium(RPE), often with bony spicule pattern of intraretinal pigment located in the midperiphery.

*A variety of clinical manifestations include:
– Cystoid macular edema, epiretinal membrane formation, optic nerve drusen.
-A Coats’-like retinal vascular response, and posterior subcapsular
cataracts. Veils, condensation and scattered pigmentary
cells may be seen in the vitreous.

*Systemic diseases may be associated with retinitis pigmentosa, and these include:
-Hearing loss, metabolic disorders, neurological syndromes,
and renal or hepatic entities.

*The typical form of retinitis pigmentosa begins with night blindness (nyctalopia) and problems with dark adaptation.

Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)
Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)

Source: 

Ophthalmology Atlas(Photos of cases)

Retinitis Pigmentosa (Generalized Rod–Cone Dystrophies)

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